Zahava C Farkas, Kevin Shayani, Shalom Z Frager, Edward Lebovics, Michelle Bravo, Larisa Debelenko and Gregory Veillette
Biliary neoplasms are rare in the pediatric population; however, botryoid variant of embryonal rhabdomyosarcoma should be considered in a young child presenting with a mass obstructing the biliary tree. Obtaining a diagnostic tissue sample and tumor management are challenging in this location. We report a case of embryonal rhabdomyosarcoma involving the common and right hepatic ducts in a female child. The diagnostic tissue sample was obtained via endoscopic retrograde cholangiopancreatography (ERCP) and Spyglass technology. The tumor was treated with right liver lobectomy following chemotherapy for control positive resection margins. The child is alive on 1 year follow up.